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1.
Rev Chil Pediatr ; 90(3): 321-327, 2019 Jun.
Artigo em Espanhol | MEDLINE | ID: mdl-31344193

RESUMO

INTRODUCTION: Adrenal masses are uncommon in newborns. The differential diagnosis includes be nign masses (adrenal hemorrhage, extralobar pulmonary sequestration) and malignant ones (neuro blastoma) that may be a finding during an obstetric ultrasound. The use of complementary imaging methods allows a better diagnosis approach during the postnatal period, with implications for the management of these patients. OBJECTIVE: To report the case of a female newborn with diagnosis of an adrenal mass, and to discuss differential diagnoses and management alternatives of adrenal lesions in newborns. CASE REPORT: Two-month-old female infant, referred for adrenal tumor study diagnosed at 22 weeks gestational age. Postnatal ultrasound showed a tumor compatible with neuroblastoma. The patient was asymptomatic, and the laboratory studies showed no relevant findings. The lesion was excised by laparoscopy. A histological study confirmed pulmonary sequestration. CONCLUSIONS: Extralobar pulmonary sequestration should be considered in the differential diagnosis of an adrenal mass in the newborn. Minimally invasive surgery should be the preferred surgical technique choice in these cases, given the technical feasibility and benefits in the recovery and cosmetic issues of the patient.


Assuntos
Neoplasias das Glândulas Suprarrenais/diagnóstico por imagem , Sequestro Broncopulmonar/diagnóstico , Neuroblastoma/diagnóstico por imagem , Neoplasias das Glândulas Suprarrenais/cirurgia , Diagnóstico Diferencial , Feminino , Humanos , Lactente , Recém-Nascido , Laparoscopia/métodos , Procedimentos Cirúrgicos Minimamente Invasivos , Neuroblastoma/cirurgia , Gravidez , Ultrassonografia , Ultrassonografia Pré-Natal
2.
Rev. chil. pediatr ; 90(3): 321-327, jun. 2019. tab, graf
Artigo em Espanhol | LILACS | ID: biblio-1013840

RESUMO

Resumen: Introducción: Las masas suprarrenales en recién nacidos son infrecuentes. El diagnóstico diferen cial incluye masas benignas (hemorragia suprarrenal o secuestro pulmonar extralobar) y malignas (neuroblastoma), y pueden ser un hallazgo durante la ecografía obstétrica. El uso de imágenes com plementarias en el periodo postnatal permite una mejor aproximación diagnóstica, con implicancias en el manejo de estos pacientes. Objetivos: comunicar el caso de una recién nacida portadora de una masa suprarrenal, discutir los diagnósticos diferenciales y el manejo de lesiones suprarrenales en recién nacidos. Caso Clínico: Lactante de 2 meses de edad, derivada para estudio de tumor supra rrenal de diagnóstico antenatal a las 22 semanas de edad gestacional. El estudio imagenológico con ecografía postnatal mostró un tumor compatible con neuroblastoma. Paciente asintomática, estudios de laboratorios sin hallazgos relevantes. Se realizó resección laparoscópica de la lesión. El estudio histológico confirmó un secuestro pulmonar. Conclusión: El secuestro pulmonar extralobar debe ser considerado en el diagnóstico diferencial de una masa suprarenal del recién nacido. La cirugía mínimamente invasiva debiera considerarse como el abordaje de elección en casos como este, donde existe factibilidad técnica y beneficios en la recuperación y secuelas cosméticas del paciente.


Abstract: Introduction: Adrenal masses are uncommon in newborns. The differential diagnosis includes be nign masses (adrenal hemorrhage, extralobar pulmonary sequestration) and malignant ones (neuro blastoma) that may be a finding during an obstetric ultrasound. The use of complementary imaging methods allows a better diagnosis approach during the postnatal period, with implications for the management of these patients. Objective: To report the case of a female newborn with diagnosis of an adrenal mass, and to discuss differential diagnoses and management alternatives of adrenal lesions in newborns. Case report: Two-month-old female infant, referred for adrenal tumor study diagnosed at 22 weeks gestational age. Postnatal ultrasound showed a tumor compatible with neuroblastoma. The patient was asymptomatic, and the laboratory studies showed no relevant findings. The lesion was excised by laparoscopy. A histological study confirmed pulmonary sequestration. Conclusions: Extralobar pulmonary sequestration should be considered in the differential diagnosis of an adrenal mass in the newborn. Minimally invasive surgery should be the preferred surgical technique choice in these cases, given the technical feasibility and benefits in the recovery and cosmetic issues of the patient.


Assuntos
Humanos , Feminino , Gravidez , Recém-Nascido , Lactente , Sequestro Broncopulmonar/diagnóstico , Neoplasias das Glândulas Suprarrenais/diagnóstico por imagem , Neuroblastoma/diagnóstico por imagem , Ultrassonografia Pré-Natal , Ultrassonografia , Laparoscopia/métodos , Neoplasias das Glândulas Suprarrenais/cirurgia , Procedimentos Cirúrgicos Minimamente Invasivos , Diagnóstico Diferencial , Neuroblastoma/cirurgia
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